E88.43
Disorders of mitochondrial tRNA synthetases
- Release
- FY 2027
- Effective
Hierarchy
Where E88.43 sits in the official hierarchy. Each level is the code it is classified under.
- E88 Other and unspecified metabolic disorders
- E88.4 Parent Mitochondrial metabolism disorders
- E88.43 This code Disorders of mitochondrial tRNA synthetases
Official Coding Notes
Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.
Inclusion Terms
ARS2-related mitochondrial disorders
Inclusion Terms
LBSL
Inclusion Terms
Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation
Inclusion Terms
Leukoencephalopathy with thalamus - brainstem involvement - high lactate
Inclusion Terms
LTBL
Inclusion Terms
Mitochondrial aminoacyl-tRNA synthetase disorders
Excludes1
disorders of pyruvate metabolism ( E74.4 )
Inherited from E88.4 — Mitochondrial metabolism disorders
Excludes1
Kearns-Sayre syndrome ( H49.81 )
Inherited from E88.4 — Mitochondrial metabolism disorders
Excludes1
histiocytosis X (chronic) ( C96.6 )
Inherited from E88 — Other and unspecified metabolic disorders
Excludes1
Leigh's encephalopathy ( G31.82 )
Inherited from E88.4 — Mitochondrial metabolism disorders
Use Additional Code
codes for associated conditions
Inherited from E88 — Other and unspecified metabolic disorders
Code Also
, if applicable, associated condition such as:
Code Also
leukoencephalopathy ( G93.49 )
Version History
How E88.43 appears in each release imported from the official files, newest first.
-
FY 2027 Effective
CurrentDisorders of mitochondrial tRNA synthetases
-
FY 2026 Effective
UnchangedDisorders of mitochondrial tRNA synthetases
Related Codes
Data Source
Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.
- Release
- FY 2027
- Effective
- Source file
- icd10cm-code-descriptions-2027.zip
Official ICD-10-CM source files (opens in a new tab)
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