E88.42
MERRF syndrome
- Release
- FY 2027
- Effective
Hierarchy
Where E88.42 sits in the official hierarchy. Each level is the code it is classified under.
- E88 Other and unspecified metabolic disorders
- E88.4 Parent Mitochondrial metabolism disorders
- E88.42 This code MERRF syndrome
Official Coding Notes
Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.
Inclusion Terms
Myoclonic epilepsy associated with ragged-red fibers
Excludes1
disorders of pyruvate metabolism ( E74.4 )
Inherited from E88.4 — Mitochondrial metabolism disorders
Excludes1
Kearns-Sayre syndrome ( H49.81 )
Inherited from E88.4 — Mitochondrial metabolism disorders
Excludes1
histiocytosis X (chronic) ( C96.6 )
Inherited from E88 — Other and unspecified metabolic disorders
Excludes1
Leigh's encephalopathy ( G31.82 )
Inherited from E88.4 — Mitochondrial metabolism disorders
Use Additional Code
codes for associated conditions
Inherited from E88 — Other and unspecified metabolic disorders
Code Also
progressive myoclonic epilepsy ( G40.3- )
Version History
How E88.42 appears in each release imported from the official files, newest first.
-
FY 2027 Effective
CurrentMERRF syndrome
-
FY 2026 Effective
UnchangedMERRF syndrome
Related Codes
Other codes under E88.4
Codes whose official notes reference E88.42
Data Source
Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.
- Release
- FY 2027
- Effective
- Source file
- icd10cm-code-descriptions-2027.zip
Official ICD-10-CM source files (opens in a new tab)
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