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ICD-10-CM Current in FY 2027

D89.44

Hereditary alpha tryptasemia

Release
FY 2027
Effective
Official source (opens in a new tab)

Hierarchy

Where D89.44 sits in the official hierarchy. Each level is the code it is classified under.

  1. D89 Other disorders involving the immune mechanism, not elsewhere classified
  2. D89.4 Parent Mast cell activation syndrome and related disorders
  3. D89.44 This code Hereditary alpha tryptasemia

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Excludes1

aggressive systemic mastocytosis ( C96.21 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

hyperglobulinemia NOS ( R77.1 )

Inherited from D89 — Other disorders involving the immune mechanism, not elsewhere classified

Excludes1

congenital cutaneous mastocytosis ( Q82.2 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

monoclonal gammopathy (of undetermined significance) ( D47.2 )

Inherited from D89 — Other disorders involving the immune mechanism, not elsewhere classified

Excludes1

(non-congenital) cutaneous mastocytosis ( D47.01 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

(indolent) systemic mastocytosis ( D47.02 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

malignant mast cell neoplasm ( C96.2- )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

malignant mastocytoma ( C96.29 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

mast cell leukemia ( C94.3- )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

mast cell sarcoma ( C96.22 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

mastocytoma NOS ( D47.09 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

other mast cell neoplasms of uncertain behavior ( D47.09 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes1

systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) ( D47.02 )

Inherited from D89.4 — Mast cell activation syndrome and related disorders

Excludes2

transplant failure and rejection ( T86 .-)

Inherited from D89 — Other disorders involving the immune mechanism, not elsewhere classified

Use Additional Code

code, if applicable, for:

Use Additional Code

allergy status, other than to drugs and biological substances ( Z91.0- )

Use Additional Code

personal history of anaphylaxis ( Z87.892 )

Version History

How D89.44 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Hereditary alpha tryptasemia

  2. FY 2026 Effective

    Unchanged

    Hereditary alpha tryptasemia

Related Codes

Other codes under D89.4

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

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