D47.02
Systemic mastocytosis
- Release
- FY 2027
- Effective
Hierarchy
Where D47.02 sits in the official hierarchy. Each level is the code it is classified under.
- D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
- D47.0 Parent Mast cell neoplasms of uncertain behavior
- D47.02 This code Systemic mastocytosis
Official Coding Notes
Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.
Inclusion Terms
Indolent systemic mastocytosis
Inclusion Terms
Isolated bone marrow mastocytosis
Inclusion Terms
Smoldering systemic mastocytosis
Inclusion Terms
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Excludes1
congenital cutaneous mastocytosis ( Q82.2 )
Inherited from D47.0 — Mast cell neoplasms of uncertain behavior
Excludes1
histiocytic neoplasms of uncertain behavior ( D47.Z9 )
Inherited from D47.0 — Mast cell neoplasms of uncertain behavior
Excludes1
malignant mast cell neoplasm ( C96.2- )
Inherited from D47.0 — Mast cell neoplasms of uncertain behavior
Excludes1
aggressive systemic mastocytosis ( C96.21 )
Excludes1
mast cell leukemia ( C94.3- )
Code Also
, if applicable, any associated hematological non-mast cell lineage disease, such as:
Code Also
chronic myelomonocytic leukemia ( C93.1- )
Code Also
essential thrombocytosis ( D47.3 )
Code Also
hypereosinophilic syndrome ( D72.1 )
Code Also
myelodysplastic syndrome ( D46.9 )
Code Also
myeloproliferative syndrome ( D47.1 )
Code Also
non-Hodgkin lymphoma (C82-C85)
Code Also
plasma cell myeloma ( C90.0- )
Code Also
polycythemia vera ( D45 )
Version History
How D47.02 appears in each release imported from the official files, newest first.
-
FY 2027 Effective
CurrentSystemic mastocytosis
-
FY 2026 Effective
UnchangedSystemic mastocytosis
Related Codes
Other codes under D47.0
Codes whose official notes reference D47.02
Data Source
Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.
- Release
- FY 2027
- Effective
- Source file
- icd10cm-code-descriptions-2027.zip
Official ICD-10-CM source files (opens in a new tab)
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