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Current

E75 Disorders of sphingolipid metabolism and other lipid storage disorders

Part of Chapter 4: Endocrine, nutritional and metabolic diseases , block Metabolic disorders (E70-E88) .

Official Notes

Excludes1

mucolipidosis, types I-III (E77.0-E77.1)

Excludes1

Refsum's disease ( G60.1 )

Child Codes

Referenced By

Official notes on these codes cite E75.

FY 2027 effective October 1, 2026 · CDC NCHS and CMS