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ICD-10-CM Current in FY 2027

E75.4

Neuronal ceroid lipofuscinosis

Release
FY 2027
Effective
Official source (opens in a new tab)

Hierarchy

Where E75.4 sits in the official hierarchy. Each level is the code it is classified under.

  1. E75 Parent Disorders of sphingolipid metabolism and other lipid storage disorders
  2. E75.4 This code Neuronal ceroid lipofuscinosis

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Inclusion Terms

Batten disease

Inclusion Terms

Bielschowsky-Jansky disease

Inclusion Terms

Kufs disease

Inclusion Terms

Spielmeyer-Vogt disease

Excludes1

mucolipidosis, types I-III (E77.0-E77.1)

Inherited from E75 — Disorders of sphingolipid metabolism and other lipid storage disorders

Excludes1

Refsum's disease ( G60.1 )

Inherited from E75 — Disorders of sphingolipid metabolism and other lipid storage disorders

Version History

How E75.4 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Neuronal ceroid lipofuscinosis

  2. FY 2026 Effective

    Unchanged

    Neuronal ceroid lipofuscinosis

Related Codes

Other codes under E75

Codes whose official notes reference E75.4

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

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