E80.0
Hereditary erythropoietic porphyria
- Release
- FY 2027
- Effective
Hierarchy
Where E80.0 sits in the official hierarchy. Each level is the code it is classified under.
- E80 Parent Disorders of porphyrin and bilirubin metabolism
- E80.0 This code Hereditary erythropoietic porphyria
Official Coding Notes
Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.
Includes
defects of catalase and peroxidase
Inherited from E80 — Disorders of porphyrin and bilirubin metabolism
Inclusion Terms
Congenital erythropoietic porphyria
Inclusion Terms
Erythropoietic protoporphyria
Version History
How E80.0 appears in each release imported from the official files, newest first.
-
FY 2027 Effective
CurrentHereditary erythropoietic porphyria
-
FY 2026 Effective
UnchangedHereditary erythropoietic porphyria
Related Codes
Other codes under E80
- E80.1 Porphyria cutanea tarda Billable
- E80.2 Other and unspecified porphyria
- E80.3 Defects of catalase and peroxidase Billable
- E80.4 Gilbert syndrome Billable
- E80.5 Crigler-Najjar syndrome Billable
- E80.6 Other disorders of bilirubin metabolism Billable
- E80.7 Disorder of bilirubin metabolism, unspecified Billable
Codes whose official notes reference E80.0
Data Source
Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.
- Release
- FY 2027
- Effective
- Source file
- icd10cm-code-descriptions-2027.zip
Official ICD-10-CM source files (opens in a new tab)
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