MedCodeSearch
ICD-10-CM Current in FY 2027

E78.010

Homozygous familial hypercholesterolemia [HoFH]

Release
FY 2027
Effective

Hierarchy

Where E78.010 sits in the official hierarchy. Each level is the code it is classified under.

  1. E78 Disorders of lipoprotein metabolism and other lipidemias
  2. E78.0 Pure hypercholesterolemia
  3. E78.01 Parent Familial hypercholesterolemia
  4. E78.010 This code Homozygous familial hypercholesterolemia [HoFH]

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Excludes1

sphingolipidosis (E75.0-E75.3)

Inherited from E78 — Disorders of lipoprotein metabolism and other lipidemias

Version History

How E78.010 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Homozygous familial hypercholesterolemia [HoFH]

  2. FY 2026 Effective

    Unchanged

    Homozygous familial hypercholesterolemia [HoFH]

Other codes under E78.01

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

MedCodeSearch is an independent reference service and is not affiliated with CMS, CDC, or the U.S. government.

Look up another code

Search ICD-10-CM, ICD-10-PCS and HCPCS Level II by code or description.