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ICD-10-CM Current in FY 2027

E75.241

Niemann-Pick disease type B

Release
FY 2027
Effective
Official source (opens in a new tab)

Hierarchy

Where E75.241 sits in the official hierarchy. Each level is the code it is classified under.

  1. E75 Disorders of sphingolipid metabolism and other lipid storage disorders
  2. E75.2 Other sphingolipidosis
  3. E75.24 Parent Niemann-Pick disease
  4. E75.241 This code Niemann-Pick disease type B

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Inclusion Terms

Acid sphingomyelinase deficiency type B (ASMD type B)

Inclusion Terms

Chronic visceral acid sphingomyelinase deficiency

Excludes1

adrenoleukodystrophy [Addison-Schilder] ( E71.528 )

Inherited from E75.2 — Other sphingolipidosis

Excludes1

mucolipidosis, types I-III (E77.0-E77.1)

Inherited from E75 — Disorders of sphingolipid metabolism and other lipid storage disorders

Excludes1

Refsum's disease ( G60.1 )

Inherited from E75 — Disorders of sphingolipid metabolism and other lipid storage disorders

Version History

How E75.241 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Niemann-Pick disease type B

  2. FY 2026 Effective

    Unchanged

    Niemann-Pick disease type B

Related Codes

Other codes under E75.24

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

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