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ICD-10-CM Current in FY 2027

E74.02

Pompe disease

Release
FY 2027
Effective
Official source (opens in a new tab)

Hierarchy

Where E74.02 sits in the official hierarchy. Each level is the code it is classified under.

  1. E74 Other disorders of carbohydrate metabolism
  2. E74.0 Parent Glycogen storage disease
  3. E74.02 This code Pompe disease

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Inclusion Terms

Cardiac glycogenosis

Inclusion Terms

Type II glycogen storage disease

Excludes1

diabetes mellitus (E08-E13)

Inherited from E74 — Other disorders of carbohydrate metabolism

Excludes1

hypoglycemia NOS ( E16.2 )

Inherited from E74 — Other disorders of carbohydrate metabolism

Excludes1

increased secretion of glucagon ( E16.3 )

Inherited from E74 — Other disorders of carbohydrate metabolism

Excludes1

mucopolysaccharidosis (E76.0-E76.3)

Inherited from E74 — Other disorders of carbohydrate metabolism

Version History

How E74.02 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Pompe disease

  2. FY 2026 Effective

    Unchanged

    Pompe disease

Related Codes

Other codes under E74.0

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

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