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ICD-10-CM Current in FY 2027

E71.311

Medium chain acyl CoA dehydrogenase deficiency

Release
FY 2027
Effective
Official source (opens in a new tab)

Hierarchy

Where E71.311 sits in the official hierarchy. Each level is the code it is classified under.

  1. E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
  2. E71.3 Disorders of fatty-acid metabolism
  3. E71.31 Parent Disorders of fatty-acid oxidation
  4. E71.311 This code Medium chain acyl CoA dehydrogenase deficiency

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Inclusion Terms

MCAD deficiency

Excludes1

peroxisomal disorders ( E71.5 )

Inherited from E71.3 — Disorders of fatty-acid metabolism

Excludes1

Refsum's disease ( G60.1 )

Inherited from E71.3 — Disorders of fatty-acid metabolism

Excludes1

Schilder's disease ( G37.0 )

Inherited from E71.3 — Disorders of fatty-acid metabolism

Excludes2

carnitine deficiency due to inborn error of metabolism ( E71.42 )

Inherited from E71.3 — Disorders of fatty-acid metabolism

Version History

How E71.311 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Medium chain acyl CoA dehydrogenase deficiency

  2. FY 2026 Effective

    Unchanged

    Medium chain acyl CoA dehydrogenase deficiency

Related Codes

Other codes under E71.31

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

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