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ICD-10-CM Current in FY 2027

E25.0

Congenital adrenogenital disorders associated with enzyme deficiency

Release
FY 2027
Effective

Hierarchy

Where E25.0 sits in the official hierarchy. Each level is the code it is classified under.

  1. E25 Parent Adrenogenital disorders
  2. E25.0 This code Congenital adrenogenital disorders associated with enzyme deficiency

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Includes

adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis

Inherited from E25 — Adrenogenital disorders

Includes

Female adrenal pseudohermaphroditism

Inherited from E25 — Adrenogenital disorders

Includes

Female heterosexual precocious pseudopuberty

Inherited from E25 — Adrenogenital disorders

Includes

Male isosexual precocious pseudopuberty

Inherited from E25 — Adrenogenital disorders

Includes

Male macrogenitosomia praecox

Inherited from E25 — Adrenogenital disorders

Includes

Male sexual precocity with adrenal hyperplasia

Inherited from E25 — Adrenogenital disorders

Includes

Male virilization (female)

Inherited from E25 — Adrenogenital disorders

Inclusion Terms

Congenital adrenal hyperplasia

Inclusion Terms

21-Hydroxylase deficiency

Inclusion Terms

Salt-losing congenital adrenal hyperplasia

Excludes1

indeterminate sex and pseudohermaphroditism ( Q56 )

Inherited from E25 — Adrenogenital disorders

Excludes1

chromosomal abnormalities (Q90-Q99)

Inherited from E25 — Adrenogenital disorders

Version History

How E25.0 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Congenital adrenogenital disorders associated with enzyme deficiency

  2. FY 2026 Effective

    Unchanged

    Congenital adrenogenital disorders associated with enzyme deficiency

Other codes under E25

Codes whose official notes reference E25.0

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

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