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ICD-10-CM Current in FY 2027

D81.818

Other biotin-dependent carboxylase deficiency

Release
FY 2027
Effective
Official source (opens in a new tab)

Hierarchy

Where D81.818 sits in the official hierarchy. Each level is the code it is classified under.

  1. D81 Combined immunodeficiencies
  2. D81.8 Other combined immunodeficiencies
  3. D81.81 Parent Biotin-dependent carboxylase deficiency
  4. D81.818 This code Other biotin-dependent carboxylase deficiency

Official Coding Notes

Reproduced verbatim from the FY 2027 ICD-10-CM files. Notes labelled as inherited are declared on a parent code and apply here too.

Inclusion Terms

Holocarboxylase synthetase deficiency

Inclusion Terms

Other multiple carboxylase deficiency

Excludes1

autosomal recessive agammaglobulinemia (Swiss type) ( D80.0 )

Inherited from D81 — Combined immunodeficiencies

Excludes1

biotin-dependent carboxylase deficiency due to dietary deficiency of biotin ( E53.8 )

Inherited from D81.81 — Biotin-dependent carboxylase deficiency

Version History

How D81.818 appears in each release imported from the official files, newest first.

  1. FY 2027 Effective

    Current

    Other biotin-dependent carboxylase deficiency

  2. FY 2026 Effective

    Unchanged

    Other biotin-dependent carboxylase deficiency

Related Codes

Other codes under D81.81

Data Source

Code information on this page is derived from the FY 2027 ICD-10-CM files published by CDC NCHS and CMS.

Release
FY 2027
Effective
Source file
icd10cm-code-descriptions-2027.zip

Official ICD-10-CM source files (opens in a new tab)

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